American Journal of Otolaryngology - Head and Neck Medicine and Surgery
Volume 27, Issue 1 , Pages 33-38 , January 2006

Characteristics of sensorineural hearing loss in children with inner ear anomalies

  • James M. Coticchia, MD

      Affiliations

    • Department of Otolaryngology Head and Neck Surgery, Wayne State University School of Medicine, Detroit, Mich, USA
    • Corresponding Author InformationCorresponding author. Department of Otolaryngology Head and Neck Surgery, Wayne State University, School of Medicine, 540 E. Canfield Avenue, 5E-UHC, Detroit, MI 48202, USA. Tel.: +1 313 577 0805; fax: +1 313 577 8555.
    • ,
  • Abhay Gokhale

      Affiliations

    • Tufts University School of Medicine, Northwestern University, Feinberg School of Medicine, Boston, Mass, USA
    • ,
  • Josh Waltonen, MD

      Affiliations

    • Department of Otolaryngology Head and Neck Surgery, Northwestern University, Feinberg School of Medicine, Chicago, Ill, USA
    • ,
  • Baran Sumer, MD

      Affiliations

    • Department of Otolaryngology Head and Neck Surgery, Washington University School of Medicine, St Louis, Mo, USA

Received 18 February 2005

References 

  1. Billings KR, Kenna MA. Causes of pediatric sensorineural hearing loss. Arch Otolaryngol Head Neck Surg. 1999;125:517–521[1986;314:1676-1686]
  2. del Castillo I, Villamar M, Moreno-Pelayo MA, et al. A deletion involving the Connexin 30 gene in nonsyndromic hearing impairment. N Engl J Med. 2002;364:243–249
  3. Willems PJ. Genetic causes of hearing loss. N Engl J Med. 2000;342:1101–1109
  4. Belal A. Usher's syndrome (retinitis pigmentosa and deafness). A temporal bone report. J Laryngol Otol. 1975;89:175–181
  5. Abe S, Usami S, Hoover DM, et al. Fluctuating sensorineural hearing loss associated with enlarged vestibular aqueduct maps to 7q31, the region containing the Pendred gene. Am J Med Genet. 1999;82:322–328
  6. Cross NC, Stephens SD, Francis M, et al. Computed tomography evaluation of the inner ear as a diagnostic, counseling and management strategy in patients with congenital sensorineural hearing impairment. Clin Otolaryngol. 1999;24:235–238
  7. Davidson HC. Imaging evaluation of sensorineural hearing loss. Semin Ultrasound CT MR. 2001;22:229–249
  8. Jackler RK, Luxford WM, House WF. Congenital malformations of the inner ear: a classification based on embryogenesis. Laryngoscope. 1987;97(Suppl 4):2–14
  9. Maniglia AM. Embryology, teratology, and arrested developmental disorders in otolaryngology. Otolaryngol Clin North Am. 1981;14:25–38
  10. Mawson SR. Diseases of the ear. 2nd ed.. London: Edward Arnold Ltd; 1968;
  11. Graham JM, Phelps PD, Michaels L. Congenital malformations of the ear and cochlear implantation in children: review and temporal bone report of common cavity. J Laryngol Otol. 2000;144(Suppl 25):1–14
  12. Zalzal GH, Tomaski SM, Vezina LG, et al. Enlarged vestibular aqueduct and sensorineural hearing loss in childhood. Arch Otolaryngol Head Neck Surg. 1995;121:23–28
  13. Valvassori GE, Clemis JD. The large vestibular aqueduct syndrome. Laryngoscope. 1978;88:723–728
  14. Levenson MJ, Parisier SC, Jacobs M, et al. The large vestibular aqueduct syndrome in children. Arch Otolaryngol Head Neck Surg. 1989;115:54–58
  15. Bamiou DE, Savy L, O'Mahoney C, et al. Unilateral sensorineural hearing loss and its aetiology in childhood: the contribution of computerized tomography in aetiological diagnosis and management. Int J Pediatr Otorhinolaryngol. 1999;51:91–99
  16. Berrettini S, Ravecca F, Sellari-Franceschini S, et al. Progressive sensorineural hearing loss in children. Pediatr Neurol. 1999;20:130–136
  17. Rupa V, Rajshekhar V, Weider DJ. Syndrome of recurrent meningitis due to congenital perilymph fistula with two different clinical presentations. Int J Pediatr Otorhinolaryngol. 2000;54:173–177

PII: S0196-0709(05)00133-X

doi: 10.1016/j.amjoto.2005.07.004

American Journal of Otolaryngology - Head and Neck Medicine and Surgery
Volume 27, Issue 1 , Pages 33-38 , January 2006

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